Abstract Gorlin syndrome, also known as nevoid basal cell carcinoma syndrome (NBCCS), is a hereditary condition transmitted as an autosomal dominant trait with high penetrance and variable expressivity. The syndrome is characterized by numerous manifestations: basal cell carcinomas (BCCs) and odontogenic keratocysts (OKCs) are the leading ones. In this article a typical Gorlin syndrome case associated with basal cell carcinoma of the vulva is described.
|Titolo:||Gorlin syndrome associated with basal cell carcinoma of the vulva: a case report|
|Autori interni:||GIULIANI, Maurizio|
DI STEFANO, LEONARDO
|Data di pubblicazione:||2006|
|Rivista:||EUROPEAN JOURNAL OF GYNAECOLOGICAL ONCOLOGY|
|Appare nelle tipologie:||1.1 Articolo in rivista|