A rare case of bilateral persistent primitive hyperplastic vitreous - MR study and follow-up

We describe the magnetic resonance features of a rare case of bilateral persistent primitive vitreous. After an initial MR scan, a follow-tip investigation disclosed a stationary picture. Thanks to its multiplanar features, MR allowed the correct identification and characterization of the malformation together with its associated endobulbar changes. The exceptional presence of a bilateral lesion, described in very few literature reports, makes the diagnosis difficult on a clinical basis. Current neuroradiological techniques offer crucial diagnostic support and allow, differential diagnosis. Technical know-how and a knowledge of the symptoms of this disease are essential.