MASTROBERARDINO, PIER GIORGIO

MASTROBERARDINO, PIER GIORGIO  

Dipartimento di Medicina clinica, sanità pubblica, scienze della vita e dell'ambiente  

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The use of progeroid DNA repair-deficient mice for assessing anti-aging compounds, illustrating the benefits of nicotinamide riboside 1-gen-2022 Birkisdóttir, María B; van Galen, Ivar; Brandt, Renata M C; Barnhoorn, Sander; van Vliet, Nicole; van Dijk, Claire; Nagarajah, Bhawani; Imholz, Sandra; van Oostrom, Conny T; Reiling, Erwin; Gyenis, Ákos; Mastroberardino, Pier G; Jaarsma, Dick; van Steeg, Harry; Hoeijmakers, Jan H J; Dollé, Martijn E T; Vermeij, Wilbert P
The PSI Domain of the MET Oncogene Encodes a Functional Disulfide Isomerase Essential for the Maturation of the Receptor Precursor 1-gen-2022 Altintas, Dogus Murat; Gallo, Simona; Basilico, Cristina; Cerqua, Marina; Bocedi, Alessio; Vitacolonna, Annapia; Botti, Orsola; Casanova, Elena; Rancati, Ilaria; Milanese, Chiara; Notari, Sara; Gambardella, Giorgia; Ricci, Giorgio; Mastroberardino, Pier Giorgio; Boccaccio, Carla; Crepaldi, Tiziana; Comoglio, Paolo Maria
PML-controlled responses in severe congenital neutropenia with ELANE-misfolding mutations 1-gen-2021 Olofsen, Patricia A; Bosch, Dennis A; Roovers, Onno; van Strien, Paulina M H; de Looper, Hans W J; Hoogenboezem, Remco M; Barnhoorn, Sander; Mastroberardino, Pier G; Ghazvini, Mehrnaz; van der Velden, Vincent H J; Bindels, Eric M J; de Pater, Emma M; Touw, Ivo P
Generation, characterization, and drug sensitivities of 12 patient-derived IDH1-mutant glioma cell cultures 1-gen-2021 Verheul, Cassandra; Ntafoulis, Ioannis; Kers, Trisha V; Hoogstrate, Youri; Mastroberardino, Pier G; Barnhoorn, Sander; Payán-Gómez, César; Tching Chi Yen, Romain; Struys, Eduard A; Koolen, Stijn L W; Dirven, Clemens M F; Leenstra, Sieger; French, Pim J; Lamfers, Martine L M
TWIST1 controls cellular senescence and energy metabolism in mesenchymal stem cells 1-gen-2021 Voskamp, C; Anderson, L A; Koevoet, W J; Barnhoorn, S; Mastroberardino, P G; van Osch, G J; Narcisi, R
The interplay between mitochondrial functionality and genome integrity in the prevention of human neurologic diseases 1-gen-2021 D'Errico, Mariarosaria; Parlanti, Eleonora; Pascucci, Barbara; Filomeni, Giuseppe; Mastroberardino, Pier Giorgio; Dogliotti, Eugenia
The Coming of Age for Big Data in Systems Radiobiology, an Engineering Perspective 1-gen-2020 Karapiperis, Christos; Chasapi, Anastasia; Angelis, Lefteris; Scouras, Zacharias G; Mastroberardino, Pier G; Tapio, Soile; Atkinson, Michael J; Ouzounis, Christos A
Gender biased neuroprotective effect of Transferrin Receptor 2 deletion in multiple models of Parkinson’s disease 1-gen-2020 Milanese, C.; Gabriels, S.; Barnhoorn, S.; Cerri, S.; Ulusoy, A.; Gornati, S. V.; Wallace, D. F.; Blandini, F.; Di Monte, D. A.; Subramaniam, V. N.; Mastroberardino, P. G.
A perspective on DNA damage-induced potentiation of the pentose phosphate shunt and reductive stress in chemoresistance 1-gen-2020 Milanese, C.; Mastroberardino, P. G.
TMX2 Is a Crucial Regulator of Cellular Redox State, and Its Dysfunction Causes Severe Brain Developmental Abnormalities 1-gen-2019 Vandervore, L. V.; Schot, R.; Milanese, C.; Smits, D. J.; Kasteleijn, E.; Fry, A. E.; Pilz, D. T.; Brock, S.; Borklu-Yucel, E.; Post, M.; Bahi-Buisson, N.; Sanchez-Soler, M. J.; van Slegtenhorst, M.; Keren, B.; Afenjar, A.; Coury, S. A.; Tan, W. -H.; Oegema, R.; de Vries, L. S.; Fawcett, K. A.; Nikkels, P. G. J.; Bertoli-Avella, A.; Al Hashem, A.; Alwabel, A. A.; Tlili-Graiess, K.; Efthymiou, S.; Zafar, F.; Rana, N.; Bibi, F.; Houlden, H.; Maroofian, R.; Person, R. E.; Crunk, A.; Savatt, J. M.; Turner, L.; Doosti, M.; Karimiani, E. G.; Saadi, N. W.; Akhondian, J.; Lequin, M. H.; Kayserili, H.; van der Spek, P. J.; Jansen, A. C.; Kros, J. M.; Verdijk, R. M.; Milosevic, N. J.; Fornerod, M.; Mastroberardino, P. G.; Mancini, G. M. S.
Peripheral mitochondrial function correlates with clinical severity in idiopathic Parkinson's disease 1-gen-2019 Milanese, Chiara; Payán-Gómez, César; Galvani, Marta; Molano González, Nicolás; Tresini, Maria; Nait Abdellah, Soraya; van Roon-Mom, Willeke M C; Figini, Silvia; Marinus, Johan; van Hilten, Jacobus J; Mastroberardino, Pier G
Endocytic iron trafficking and mitochondria in Parkinson's disease 1-gen-2019 Cerri, S.; Milanese, C.; Mastroberardino, P. G.
Metabolic Alterations in Aging Macrophages: Ingredients for Inflammaging? 1-gen-2019 van Beek, Adriaan A.; Van den Bossche, Jan; Mastroberardino, Pier G.; de Winther, Menno P. J.; Leenen, Pieter J. M.
DNA damage and transcription stress cause ATP-mediated redesign of metabolism and potentiation of anti-oxidant buffering 1-gen-2019 Milanese, Chiara; Bombardieri, Cíntia R; Sepe, Sara; Barnhoorn, Sander; Payán-Goméz, César; Caruso, Donatella; Audano, Matteo; Pedretti, Silvia; Vermeij, Wilbert P; Brandt, Renata M C; Gyenis, Akos; Wamelink, Mirjam M; de Wit, Annelieke S; Janssens, Roel C; Leen, René; van Kuilenburg, André B P; Mitro, Nico; Hoeijmakers, Jan H J; Mastroberardino, Pier G
Cysteine oxidation and redox signaling in dopaminergic neurons physiology and in Parkinson's disease 1-gen-2019 Milanese, C.; Payan-Gomez, C.; Mastroberardino, P. G.
Bioenergetics in fibroblasts of patients with Huntington disease are associated with age at onset 1-gen-2018 Gardiner, Sarah L.; Milanese, Chiara; Boogaard, Merel W.; Buijsen, Ronald A. M.; Hogenboom, Marye; Roos, Raymund A. C.; Mastroberardino, Pier G.; Van Roon-Mom, Willeke M. C.; Aziz, N. Ahmad
Decreased mitochondrial respiration in aneurysmal aortas of Fibulin-4 mutant mice is linked to PGC1A regulation 1-gen-2018 van der Pluijm, Ingrid; Burger, Joyce; van Heijningen, Paula M.; Ijpma, Arne; van Vliet, Nicole; Milanese, Chiara; Schoonderwoerd, Kees; Sluiter, Willem; Ringuette, Lea-Jeanne; Dekkers, Dirk H W; Que, Ivo; Kaijzel, Erik L.; Te Riet, Luuk; Macfarlane, Elena G.; Das, Devashish; van der Linden, Reinier; Vermeij, Marcel; Demmers, Jeroen A.; Mastroberardino, Pier G.; Davis, Elaine C.; Yanagisawa, Hiromi; Dietz, Harry C.; Kanaar, Roland; Essers, Jeroen
Activation of the DNA damage response in vivo in synucleinopathy models of Parkinson’s disease 1-gen-2018 Milanese, Chiara; Cerri, Silvia; Ulusoy, Ayse; Gornati, Simona V.; Plat, Audrey; Gabriels, Sylvia; Blandini, Fabio; Di Monte, Donato A.; Hoeijmakers, Jan H.; Mastroberardino, Pier G.
Mitochondrial Complex i Reversible S-Nitrosation Improves Bioenergetics and Is Protective in Parkinson's Disease 1-gen-2018 Milanese, Chiara; Tapias, Victor; Gabriels, Sylvia; Cerri, Silvia; Levandis, Giovanna; Blandini, Fabio; Tresini, Maria; Shiva, Sruti; Greenamyre, John Timothy; Gladwin, Mark T.; Mastroberardino, Pier G.
CHAPTER 12. Genes, Aging, and Parkinson’s Disease 1-gen-2017 Milanese, Chiara; Mastroberardino, Pier G.